lvrachЛечащий ВрачLechaschi Vrach1560-51752687-1181lvrach-612Research ArticleСтатьиОценка кожных проявлений при мастоцитозе взрослых и их связь с симптомами, уровнем триптазы и подтипом заболеванияAssessment of skin manifestations under mastocytosis in adults and their associations with symptoms, level of tryptase and subtype of the diseaseТеплюкН. П.TeplyukN. P.noemail@neicon.ruПятиловаП. М.PyatilovaP. M.polinapyatilova@gmail.comФГАОУ ВО Первый МГМУ им. И. М. Сеченова МЗ РФRussian Federation2018230620210109191Copyright © Теплюк Н.П., Пятилова П.М., 20212021Теплюк Н.П., Пятилова П.М.Teplyuk N.P., Pyatilova P.M.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.lvrach.ru/jour/article/view/612

Клинические характеристики 30 взрослых больных мастоцитозом с поражением кожи были сопоставлены с длительностью заболевания, тяжестью кожных и системных симптомов, вовлечением в патологический процесс внутренних органов, уровнем триптазы в сыворотке крови и наличием поражения костного мозга. Наличие кожных и системных симптомов, а также уровень триптазы могут быть полезны для оценки степени поражения внутренних органов при мастоцитозе у взрослых.

Clinical features of 30 adult patients suffering from mastocytosis with skin lesion were compared with the duration of the disease, severity of skin and systemic symptoms, involvement of the internals in the pathologic process, level of tryptase in the blood serum and presence of marrow lesion. Presence of skin and systemic symptoms, as well as the level of tryptase, can be useful for assessment of internal lesion in mastocytosis in adults. 

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The authors declare that there are no conflicts of interest present.